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Dernières publications
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Julia Pereira Lemos, Liliane Patrícia Gonçalves Tenório, Vincent Mouly, Gillian Butler-Browne, Daniella Arêas Mendes-Da-Cruz, et al.. T cell biology in neuromuscular disorders: a focus on Duchenne Muscular Dystrophy and Amyotrophic Lateral Sclerosis. Frontiers in Immunology, 2023, 14, pp.120283. ⟨10.3389/fimmu.2023.1202834⟩. ⟨hal-04603915⟩
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
Chiffres clés
103
Publications avec texte intégral
Open Access
61 %
Mots clés
Akt
Dysferlinopathy
Gene replacement
Cell therapy
Atrophy
DUX4
Myoblasts
Differentiation
OPMD
2-D PAGE
Adipose tissue
Exon-skipping
Duchenne muscular dystrophy
Satellite cell
Lamins
AAV
AChR antibodies
Muscle stem cells
Autoimmune diseases
RNA
Autologous
Aged
Amyotrophic Lateral Sclerosis
DMD
Myotube
DNA methylation
Thérapie génique
FSHD
Geriatric assessment
APOPTOSIS
Transcriptomics
Metabolism
Actin
Regulatory T cells
Myopathy
Andermann syndrome
Neuromuscular junction NMJ
GENE
Haploinsufficiency
Gene therapy
Myogenesis
Regeneration
Skeletal muscle
ALS
Biomarker
Neuromuscular disease
Epigenetics
Annexin A2
Triplet expansion disease
Pharyngeal muscle
Dystrophie musculaire oculopharyngée
PABPN1
Muscular dystrophy
Fibrosis
BINDING SPECIFICITY
Muscle strength
Pax7
Myositis
Effector T cells
FAPs
AAV vectors
Oculopharyngeal muscular dystrophy
Calcium
Aav-U7
Muscle fibrosis
Intercellular communication
Ageing
Mass spectrometry
Anti-acetylcholine receptor antibodies
Myoblast
PABPN1 agregates
Antiserum
Cross-bridge kinetics
AUTOPHAGY
Inflammation
Satellite cells
Omics
Anti-fibrotic pharmacotherapies
Arbovirus
Regenerative medicine
Dysferlin
Antisens oligonucleotides
Myosin
Functional genomics
ARN
Muscle
Agrégats de PABPN1
Aggregate
MUTATIONS
Xenograft
Sarcopenia
Nuclear envelope
Bile salt hydrolases
Human
Accelerometry
Muscle dystrophy
Alphavirus
Myopathies
Dystrophin
Alzheimer's disease